Sarcoma
From Anvita Health Wiki
Contents |
More Specific Terms
- alveolar soft part sarcoma
- chondrosarcoma
- clear cell sarcoma of tendons & aponeuroses (malignant melanoma of soft parts)
- desmoplastic small round cell tumor (DSRCT)
- epithelioid sarcoma
- Ewing's sarcoma
- fibromyxoid sarcoma
- fibrosarcoma
- gliosarcoma
- hemangiosarcoma
- Kaposi's sarcoma
- leiomyosarcoma
- liposarcoma
- lymphangiosarcoma
- malignant fibrous histiocytoma (MFH, angiomatoid fibrous histiocytoma)
- malignant peripheral nerve sheath tumor (MPNST)
- mast cell sarcoma
- mesothelioma
- myeloid sarcoma (extramedullary myeloid tumor, granulocytic sarcoma, chloroma)
- osteosarcoma (osteogenic sarcoma)
- rhabdoid tumor
- rhabdomyosarcoma (Sarcoma Botryoides)
- round cell sarcomas
- soft tissue sarcoma
- synovial sarcoma
Genetics
- implicated genes: CTDSP2
Complications
Management
-
- 2 cm margins is optimal
- adjuvant therapy
- except rhabdomyosarcoma & Ewing's sarcoma
- chemotherapy may be palliative
More General Terms
References
- Medical Knowledge Self Assessment Program (MKSAP) 11, American College of Physicians, Philadelphia 1998
- National Guideline Clearinghouse Improving outcomes for people with sarcoma. (National Collaborating Centre for Cancer) ngc-guideline:9002
